Table 2 The deafness gene detected in this cohort

1

GJB2

71

34

TRRAP

3

67

GAB1

1

2

SLC26A4

51

35

ADGRV1

3

68

CREBBP

1

3

MYO15A

22

36

FGFR3

2

69

FOXC1

1

4

MYO7A

21

37

MT-RNR1

2

70

CLDN14

1

5

TMC1

13

38

GATA3

2

71

COL1A1

1

6

CDH23

14

39

SALL4

2

72

COL9A1

1

7

MITF

13

40

POU3F4

2

73

TRPV4

1

8

USH2A

13

41

CHD7

2

74

FLNB

1

9

WFS1

11

42

TSHZ1

2

75

COL2A1

1

10

COL11A2

10

43

MYO6

2

76

HOMER2

1

11

OTOF

10

44

COL4A6

2

77

LARS2

1

12

SOX10

10

45

USH1G

2

78

DSPP

1

13

PTPN11

8

46

DIAPH3

2

79

CLRN1

1

14

OTOG

6

47

EYA4

2

80

SH3TC2

1

15

TNC

6

48

DIAPH1

2

81

MARVELD2

1

16

EYA1

5

49

EDNRB

1

82

P2RX2

1

17

GJB3

5

50

PRPS1

1

83

SIX5

1

18

TECTA

5

51

ESRRB

1

84

CEACAM16

1

19

BDP1

4

52

ACTG1

1

85

TBL1Y

1

20

USH1C

4

53

GRXCR1

1

86

YAP1

1

21

PTPRQ

4

54

ACTB

1

87

CABP2

1

22

TRIOBP

4

55

TWIST1

1

88

CD164

1

23

MYO1A

4

56

PDE1C

1

89

GSDME

1

24

PCDH15

4

57

TMIE

1

90

MYH14

1

25

WHRN

4

58

ANKRD11

1

91

TCOF1

1

26

DMXL2

3

59

AIFM1

1

92

POLG

1

27

MYH9

3

60

TPRN

1

93

NLRP3

1

28

LHFPL5

3

61

PDZD7

1

94

REST

1

29

MCM2

3

62

FLNA

1

95

PAX3

1

30

TBC1D24

3

63

BCOR

1

96

KCNQ4

1

31

COL11A1

3

64

TNFRSF11A

1

97

COL4A5

1

32

LOXHD1

3

65

LRP2

1

98

CCDC50

1

33

SLC17A8

3

66

ERCC6

1